Dermatomiositis hipomiopática asociada con enfermedad pulmonar intersticial rápidamente progresiva complicada con neumomediastino: una revisión basada en casos

Translated title of the contribution: Rapidly progressive interstitial lung disease-associated hypomyopathic dermatomyositis complicated with pneumomediastinum: A case-based review

Julio Alejandro Cerna-López, Paul J. Tejada-Llacsa, Fiorella Andrea de Jesús Valle-Farfán, Graciela S. Alarcón, Manuel Francisco Ugarte Gil, Víctor R. Pimentel-Quiroz

Research output: Contribution to journalArticlepeer-review

Abstract

Clinically amyopathic dermatomyositis (CADM) is associated with antibodies directed against the protein encoded by the melanoma differentiation-associated gene 5 (MDA5). CADM patients have an increased risk of developing rapidly progressive interstitial lung disease (RP-ILD) and spontaneous pneumomediastinum. Two Peruvian cases of RP-ILD-associated CADM with spontaneous pneumomediastinum are presented, one of them was anti-MDA5 antibody positive. To our knowledge, this is the first report of anti-MDA5-associated CADM in the Peruvian population.

Translated title of the contributionRapidly progressive interstitial lung disease-associated hypomyopathic dermatomyositis complicated with pneumomediastinum: A case-based review
Original languageSpanish
JournalRevista Colombiana de Reumatologia
DOIs
StateAccepted/In press - 2021
Externally publishedYes

Bibliographical note

Publisher Copyright:
© 2021 Asociación Colombiana de Reumatología

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