Síndrome de Susac: primer reporte de caso en el Perú

Translated title of the contribution: Susac syndrome: the first case report in Peru

Carolina Rivadeneira-Sotelo, Maria Meza Vega, Darwin Segura-Chávez, Sheila Castro-Suarez

Research output: Contribution to journalArticlepeer-review

1 Scopus citations

Abstract

Susac Syndrome is a rare entity, characterized by a triad of subacute encephalopathy, retinal artery occlusion and sensorineural hearing loss. It is more common in women and the age of onset fluctuates between 9-58 years of age. The pathogenesis is presented as microangiopathic changes at the cerebral, retinal and cochlear levels associated with an autoimmune mechanism. We present the case of a 31-year-old woman who started with a diffuse headache, puerile behavior, bradylalia and somnolence. As the disease progressed, she had auditory deficit and arterial obstruction of the right temporal retinal branch in retinal fluorescein angiography. Brain magnetic resonance showed rounded hyperintense lesions in the corpus callosum, periventricular region and cerebellum. This is the first reported case of Susac Syndrome in Peru, presented with the classic triad, which is an infrequent presentation. However, cases that show incomplete forms should be evaluated in a timely manner to initiate timely treatment and avoid irreversible consequences.

Translated title of the contributionSusac syndrome: the first case report in Peru
Original languageSpanish
Pages (from-to)e7033
JournalMedwave
Volume17
Issue number7
DOIs
StatePublished - 30 Aug 2017
Externally publishedYes

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