Resumen
Clinically amyopathic dermatomyositis (CADM) is associated with antibodies directed against the protein encoded by the melanoma differentiation-associated gene 5 (MDA5). CADM patients have an increased risk of developing rapidly progressive interstitial lung disease (RP-ILD) and spontaneous pneumomediastinum. Two Peruvian cases of RP-ILD-associated CADM with spontaneous pneumomediastinum are presented, one of them was anti-MDA5 antibody positive. To our knowledge, this is the first report of anti-MDA5-associated CADM in the Peruvian population.
Título traducido de la contribución | Rapidly progressive interstitial lung disease-associated hypomyopathic dermatomyositis complicated with pneumomediastinum: A case-based review |
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Idioma original | Español |
Publicación | Revista Colombiana de Reumatologia |
DOI | |
Estado | Aceptada/en prensa - 2021 |
Nota bibliográfica
Publisher Copyright:© 2021 Asociación Colombiana de Reumatología
Palabras clave
- Anti-MDA5 antibodies
- Clinically amyopathic dermatomyositis
- Spontaneous pneumomediastinum