Susac syndrome: the first case report in Peru

Título traducido de la contribución: Síndrome de Susac: primer reporte de caso en el Perú

Carolina Rivadeneira-Sotelo, María Meza Vega, Darwin Segura-Chávez, Sheila Castro-Suarez

Producción científica: Contribución a una revistaArtículorevisión exhaustiva

3 Citas (Scopus)


Susac Syndrome is a rare entity, characterized by a triad of subacute encephalopathy, retinal artery occlusion and sensorineural hearing loss. It is more common in women and the age of onset fluctuates between 9-58 years of age. The pathogenesis is presented as microangiopathic changes at the cerebral, retinal and cochlear levels associated with an autoimmune mechanism. We present the case of a 31-year-old woman who started with a diffuse headache, puerile behavior, bradylalia and somnolence. As the disease progressed, she had auditory deficit and arterial obstruction of the right temporal retinal branch in retinal fluorescein angiography. Brain magnetic resonance showed rounded hyperintense lesions in the corpus callosum, periventricular region and cerebellum. This is the first reported case of Susac Syndrome in Peru, presented with the classic triad, which is an infrequent presentation. However, cases that show incomplete forms should be evaluated in a timely manner to initiate timely treatment and avoid irreversible consequences.

Título traducido de la contribuciónSíndrome de Susac: primer reporte de caso en el Perú
Idioma originalInglés
Páginas (desde-hasta)e7033
EstadoPublicada - 30 ago. 2017
Publicado de forma externa


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