Síndrome de Susac: primer reporte de caso en el Perú

Carolina Rivadeneira-Sotelo, Maria Meza Vega, Darwin Segura-Chávez, Sheila Castro-Suarez

Resultado de la investigación: Contribución a una revistaArtículorevisión exhaustiva

2 Citas (Scopus)

Resumen

Susac Syndrome is a rare entity, characterized by a triad of subacute encephalopathy, retinal artery occlusion and sensorineural hearing loss. It is more common in women and the age of onset fluctuates between 9-58 years of age. The pathogenesis is presented as microangiopathic changes at the cerebral, retinal and cochlear levels associated with an autoimmune mechanism. We present the case of a 31-year-old woman who started with a diffuse headache, puerile behavior, bradylalia and somnolence. As the disease progressed, she had auditory deficit and arterial obstruction of the right temporal retinal branch in retinal fluorescein angiography. Brain magnetic resonance showed rounded hyperintense lesions in the corpus callosum, periventricular region and cerebellum. This is the first reported case of Susac Syndrome in Peru, presented with the classic triad, which is an infrequent presentation. However, cases that show incomplete forms should be evaluated in a timely manner to initiate timely treatment and avoid irreversible consequences.

Título traducido de la contribuciónSusac syndrome: the first case report in Peru
Idioma originalEspañol
Páginas (desde-hasta)e7033
PublicaciónMedwave
Volumen17
N.º7
DOI
EstadoPublicada - 30 ago. 2017
Publicado de forma externa

Palabras clave

  • autoimmune endotheliopathy
  • hearing loss
  • microangiopathy
  • retinocochleocerebral vasculopathy
  • Susac syndrome
  • encephalopathy

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